Rapidly Progressive Dementia
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Neurodegenerative Diseases and Prions
NEJM 344:1516-1526,1548, Prusiner,S.B., 2001
The Polymerase Chain Reaction:Application to Nervous System Disease
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Criteria for the Diagnosis of Corticobasal Degeneration
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Differential Diagnosis of Bilateral Abnormalities of the Basal Ganglia and Thalamus
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Parkinsonism in HIV-Infected Patients on Highly Active Antiretroviral Therapy
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Neuroimaging Findings in Human Prion Disease
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Consequences of the Delayed Diagnosis of Ataxia-Telangiectasia
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A New Variant of Creutzfeldt-Jakob Disease in the UK
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Chronic Neurodegenerative Disease Associated with HTLV-II Infection
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MR Imaging of the Spinal Cord:Current Status and Futue Advances
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Mutation of the Prion Protein in Libyan Jews with Creutzfeldt-Jakob Disease
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Rapid Detection of Creutzfeldt-Jakob Disease and Scrapie Prion Porteins
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Prions & Neurodegenerative Diseases
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Cognitive and Clinical Characteristics of Patients with Limbic-Predominant Age-Related TDP-43 Encephalopathy
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Fragile X-Associated Tremor or Ataxia Syndrome in a Patient with Difficulty Walking, Falls, a Tremor, and Erectile Dysfunction
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Sport Associated Dementia
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Single Photon Emission Computed Tomography/Positron Emission Tomography Molecular Imaging for Parkinsonism: A Fast-Developing Field
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Clinicopathologic conference, Frontotemporal Lobar Degeneration with tau-positive inclusions consistent with Picks disease
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Stridor in Multiple System Atrophy
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Neurodegenerative Disease Mortality Among Former Professional Soccer Players
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Hereditary Spastic Paraplegia:From Diagnosis to Emerging Therapeutic Approaches
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Atypical Parkinsonian Syndromes: A General Neurologists Perspective
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Pantothenate Kinase - Associated Neurodegeneration (PKAN)
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Clinicopathologic Conference, Primary Progressive Aphasia, Semantic Variant, due to TAR DNA Binding Protein 43 associated Frontotemporal Lobar Degen
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Amyotrophic Lateral Sclerosis
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Dentate Update: Imaging Features of Entities that Affect the Dentate Nucleus
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Neuroimaging Changes in Menkes Disease, Part 1
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Intrathecal 2-hydroxypropyl-�-cyclodextrin Decreases Neurological Disease Progression in Niemann-Pick disease, type C1: a non-randomised, open-label, phase 1-2 trial
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A Case of Ataxia, Seizure, and Choreoathetosis in a 34-year-old Woman
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Leukodystrophy and Progressive Myoclonic Epilepsy Disclosing DRPLA
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Orthostatic Myoclonus Associated with CASPR2 Antibodies
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A Young Man with Progressive Language Difficulty and Early-Onset Dementia
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Multiple-System Atrophy
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Clinicopathologic Conference, Frontotemporal Lobar Degeneration with Tau-positive Inclusions (Picks Disease Subtype) Due to a Gly389Arg MAPT Mutation, Resulting in the Behavioral Variant of Frontotemporal Dementia with Parkinsonism
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Clinical Reasoning: A Woman with Rapidly Progressive Apraxia
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Ataxia, Dementia, and Hypogonadotropism Caused by Disordered Ubiquitination
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Inverse Association between Cancer and Alzheimers Disease: Results from the Framingham Heart Study
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Neurodegenerative causes of death among retired National Football League Players
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Treatment of Multiple System Atrophy Using Intravenous Immunoglobulin
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Clinicopathologic Conference, Kufs Disease (Autosomal Dominant) Parry Type Neuronal Ceroid Lypofuscinosis
NEJM 364:1062-1074, Case 8-2011, 2011
Skin biopsy is useful for the antemortem diagnosis of neuronal intranuclear inclusion disease
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The Spectrum of Mutations in Progranulin: A Collaborative Study Screening 545 Cases of Neurodegeneration
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Huntingtons Disease
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Rapidly Progressive Neurodegenerative Dementias
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A 75-Year-Old Woman with Progressive Right-Hand Tremor and Inability to Use Her Right Side
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